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Number of items: 5.

Journal Article

Pollmann, Charlotte, Haug, Michael, Reischl, Barbara, Proelss, Gerhard, Poeschel, Thorsten, Rupitsch, Stefan J., Clemen, Christoph S., Schroeder, Rolf and Friedrich, Oliver ORCID: 0000-0003-2238-2049 (2020). Growing Old Too Early: Skeletal Muscle Single Fiber Biomechanics in Ageing R349P Desmin Knock-in Mice Using the MyoRobot Technology. Int. J. Mol. Sci., 21 (15). BASEL: MDPI. ISSN 1422-0067

Haug, Michael, Meyer, Charlotte, Reischl, Barbara, Proelss, Gerhard, Vetter, Kristina, Iberl, Julian, Nuebler, Stefanie, Schuermann, Sebastian, Rupitsch, Stefan J., Heckel, Michael, Poeschel, Thorsten, Winter, Lilli ORCID: 0000-0002-6368-1160, Herrmann, Harald, Clemen, Christoph S., Schroeder, Rolf and Friedrich, Oliver ORCID: 0000-0003-2238-2049 (2019). The MyoRobot technology discloses a premature biomechanical decay of skeletal muscle fiber bundles derived from R349P desminopathy mice. Sci Rep, 9. LONDON: NATURE PUBLISHING GROUP. ISSN 2045-2322

Diermeier, Stefanie, Iberl, Julian, Vetter, Kristina, Haug, Michael, Pollmann, Charlotte, Reischl, Barbara, Buttgereit, Andreas, Schuermann, Sebastian, Spoerrer, Marina, Goldmann, Wolfgang H., Fabry, Ben ORCID: 0000-0003-1737-0465, Elhamine, Fatiha, Stehle, Robert, Pfitzer, Gabriele, Winter, Lilli ORCID: 0000-0002-6368-1160, Clemen, Christoph S., Herrmann, Harald, Schroeder, Rolf and Friedrich, Oliver ORCID: 0000-0003-2238-2049 (2017). Early signs of architectural and biomechanical failure in isolated myofibers and immortalized myoblasts from desmin-mutant knock-in mice. Sci Rep, 7. LONDON: NATURE PUBLISHING GROUP. ISSN 2045-2322

Diermeier, Stefanie, Buttgereit, Andreas, Schuermann, Sebastian, Winter, Lilli ORCID: 0000-0002-6368-1160, Xu, Hongyang, Murphy, Robyn M., Clemen, Christoph S., Schroeder, Rolf and Friedrich, Oliver ORCID: 0000-0003-2238-2049 (2017). Preaged remodeling of myofibrillar cytoarchitecture in skeletal muscle expressing R349P mutant desmin. Neurobiol. Aging, 58. S. 77 - 88. NEW YORK: ELSEVIER SCIENCE INC. ISSN 1558-1497

Clemen, Christoph S., Stoeckigt, Florian, Strucksberg, Karl-Heinz, Chevessier, Frederic, Winter, Lilli ORCID: 0000-0002-6368-1160, Schuetz, Johanna, Bauer, Ralf, Thorweihe, Jose-Manuel, Wenzel, Daniela ORCID: 0000-0003-1100-6363, Schloetzer-Schrehardt, Ursula, Rasche, Volker, Krsmanovic, Pavle ORCID: 0000-0003-1142-4282, Katus, Hugo A., Rottbauer, Wolfgang, Just, Steffen, Mueller, Oliver J., Friedrich, Oliver ORCID: 0000-0003-2238-2049, Meyer, Rainer, Herrmann, Harald, Schrickel, Jan Wilko and Schroeder, Rolf (2015). The toxic effect of R350P mutant desmin in striated muscle of man and mouse. Acta Neuropathol., 129 (2). S. 297 - 316. NEW YORK: SPRINGER. ISSN 1432-0533

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