Joint-Preserving Therapy for Osteogenesis Imperfecta - Kölner UniversitätsPublikationsServer

Yagdiran, Ayla, Otto-Lambertz, Christina, Eysel, Peer and Semler, Oliver . Joint-Preserving Therapy for Osteogenesis Imperfecta. Osteologie. STUTTGART: GEORG THIEME VERLAG KG. ISSN 2567-5818

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DOI:10.1055/a-1982-3250

Abstract

Background Osteogenesis imperfecta (OI) is a skeletal disease with a frequency of about 1:20,000, which paediatricians and orthopaedic surgeons are rarely confronted with. Method Selective literature search in the PubMed database including case studies and reviews up to August 2022. Results Interdisciplinary cooperation between paediatricians and orthopaedic surgeons is essential for an optimal therapeutic decision for or against surgical treatment of OI. While titanium elastic nails (TENs) are still frequently used for the surgical treatment of the forearm in small children, telescopic nails are primarily used for the joint-preserving treatment of OI as soon as the diameter of the bone permits. The most commonly used telescopic nail is the Fassier-Duval (FD) nail. In adult adolescents and adults, so-called custom made implants are necessary due to the small medullary canal diameters. In the absence of postoperative primary load stability, immobilisation is indicated, which leads to further deterioration of the already atrophic muscle in the OI patient. Conclusion Despite optimisation and the development of special implants, the joint-retaining treatment of OI continues to be a challenge for both patient and doctor.

Item Type:

Journal Article

Creators:

Creators	Email	ORCID	ORCID Put Code
Yagdiran, Ayla	UNSPECIFIED	UNSPECIFIED	UNSPECIFIED
Otto-Lambertz, Christina	UNSPECIFIED	UNSPECIFIED	UNSPECIFIED
Eysel, Peer	UNSPECIFIED	UNSPECIFIED	UNSPECIFIED
Semler, Oliver	UNSPECIFIED	UNSPECIFIED	UNSPECIFIED