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Journal Article
Clemen, Christoph S., Winter, Lilli ORCID: 0000-0002-6368-1160, Strucksberg, Karl-Heinz, Berwanger, Carolin, Tuerk, Matthias, Kornblum, Cornelia, Florin, Alexandra, Aguilar-Pimentel, Juan Antonio, Amarie, Oana Veronica, Becker, Lore
ORCID: 0000-0002-6890-4984, Garrett, Lillian
ORCID: 0000-0003-4880-7076, Hans, Wolfgang, Moreth, Kristin, Neff, Frauke, Pingen, Laura, Rathkolb, Birgit, Racz, Ildika, Rozman, Jan
ORCID: 0000-0002-8035-8904, Treise, Irina, Fuchs, Helmut, Gailus-Durner, Valerie, de Angelis, Martin Hrabe
ORCID: 0000-0002-7898-2353, Vorgerd, Matthias, Eichinger, Ludwig
ORCID: 0000-0003-1594-6117 and Schroeder, Rolf
(2018).
The heterozygous R155C VCP mutation: Toxic in humans! Harmless in mice?
Biochem. Biophys. Res. Commun., 503 (4).
S. 2770 - 2778.
SAN DIEGO:
ACADEMIC PRESS INC ELSEVIER SCIENCE.
ISSN 1090-2104
Diermeier, Stefanie, Buttgereit, Andreas, Schuermann, Sebastian, Winter, Lilli ORCID: 0000-0002-6368-1160, Xu, Hongyang, Murphy, Robyn M., Clemen, Christoph S., Schroeder, Rolf and Friedrich, Oliver
ORCID: 0000-0003-2238-2049
(2017).
Preaged remodeling of myofibrillar cytoarchitecture in skeletal muscle expressing R349P mutant desmin.
Neurobiol. Aging, 58.
S. 77 - 88.
NEW YORK:
ELSEVIER SCIENCE INC.
ISSN 1558-1497
Diermeier, Stefanie, Iberl, Julian, Vetter, Kristina, Haug, Michael, Pollmann, Charlotte, Reischl, Barbara, Buttgereit, Andreas, Schuermann, Sebastian, Spoerrer, Marina, Goldmann, Wolfgang H., Fabry, Ben ORCID: 0000-0003-1737-0465, Elhamine, Fatiha, Stehle, Robert, Pfitzer, Gabriele, Winter, Lilli
ORCID: 0000-0002-6368-1160, Clemen, Christoph S., Herrmann, Harald, Schroeder, Rolf and Friedrich, Oliver
ORCID: 0000-0003-2238-2049
(2017).
Early signs of architectural and biomechanical failure in isolated myofibers and immortalized myoblasts from desmin-mutant knock-in mice.
Sci Rep, 7.
LONDON:
NATURE PUBLISHING GROUP.
ISSN 2045-2322
Haug, Michael, Meyer, Charlotte, Reischl, Barbara, Proelss, Gerhard, Vetter, Kristina, Iberl, Julian, Nuebler, Stefanie, Schuermann, Sebastian, Rupitsch, Stefan J., Heckel, Michael, Poeschel, Thorsten, Winter, Lilli ORCID: 0000-0002-6368-1160, Herrmann, Harald, Clemen, Christoph S., Schroeder, Rolf and Friedrich, Oliver
ORCID: 0000-0003-2238-2049
(2019).
The MyoRobot technology discloses a premature biomechanical decay of skeletal muscle fiber bundles derived from R349P desminopathy mice.
Sci Rep, 9.
LONDON:
NATURE PUBLISHING GROUP.
ISSN 2045-2322
Winter, Lilli ORCID: 0000-0002-6368-1160, Wittig, Ilka, Peeva, Viktoriya, Eggers, Britta
ORCID: 0000-0002-6553-4631, Heidler, Juliana, Chevessier, Frederic, Kley, Rudolf A., Barkovits, Katalin, Strecker, Valentina, Berwanger, Carolin, Herrmann, Harald, Marcus, Katrin, Kornblum, Cornelia, Kunz, Wolfram S.
ORCID: 0000-0003-1113-3493, Schroeder, Rolf and Clemen, Christoph S.
(2016).
Mutant desmin substantially perturbs mitochondrial morphology, function and maintenance in skeletal muscle tissue.
Acta Neuropathol., 132 (3).
S. 453 - 474.
NEW YORK:
SPRINGER.
ISSN 1432-0533